Splenic Vein Leiomyosarcoma: Case Report and Review of the Literature

  • Damiano Patrono Department of Surgery, University of Turin. Turin, Italy
  • Luca Molinaro Department of Medical Sciences, University of Turin. Turin, Italy
  • Elena Mazza Department of Surgery, University of Turin. Turin, Italy
  • Renato Romagnoli Department of Surgery, University of Turin. Turin, Italy
  • Mauro Salizzoni Department of Surgery, University of Turin. Turin, Italy
Keywords: Leiomyosarcoma, Splenic Vein, Thrombosis


Context Primary venous leiomyosarcoma (LMS) is a rare disease, most commonly affecting the retroperitoneal veins and in particular the inferior vena cava. Five-year survival rate ranges between 33% and 68%. Case Report Complete surgical resection represents the only potentially curative treatment, occasionally achieving long-term survival. LMS of the splenic vein is extremely rare, with only three cases reported in the literature. Conclusion We report a case of primary venous LMS arising from the splenic vein and we briefly review the relevant literature.

Image: Intraoperative snapshot.


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Intraoperative snapshot
How to Cite
PatronoD., MolinaroL., MazzaE., RomagnoliR., & SalizzoniM. (2014). Splenic Vein Leiomyosarcoma: Case Report and Review of the Literature. JOP. Journal of the Pancreas, 15(5), 512-514. https://doi.org/10.6092/1590-8577/2803