Splenic Vein Leiomyosarcoma: Case Report and Review of the Literature

Damiano Patrono; Luca Molinaro; Elena Mazza; Renato Romagnoli; Mauro Salizzoni

doi:10.6092/1590-8577/2803

Damiano Patrono Department of Surgery, University of Turin. Turin, Italy
Luca Molinaro Department of Medical Sciences, University of Turin. Turin, Italy
Elena Mazza Department of Surgery, University of Turin. Turin, Italy
Renato Romagnoli Department of Surgery, University of Turin. Turin, Italy
Mauro Salizzoni Department of Surgery, University of Turin. Turin, Italy

DOI: https://doi.org/10.6092/1590-8577/2803

Keywords: Leiomyosarcoma, Splenic Vein, Thrombosis

Abstract

Context Primary venous leiomyosarcoma (LMS) is a rare disease, most commonly affecting the retroperitoneal veins and in particular the inferior vena cava. Five-year survival rate ranges between 33% and 68%. Case Report Complete surgical resection represents the only potentially curative treatment, occasionally achieving long-term survival. LMS of the splenic vein is extremely rare, with only three cases reported in the literature. Conclusion We report a case of primary venous LMS arising from the splenic vein and we briefly review the relevant literature.

Image: Intraoperative snapshot.

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