Magnetic Resonance Cholangiography with Mangafodipir Trisodium in Caroli's Disease with Pancreas Involvement

  • Simone Maurea Department of Biomorphological and Functional Sciences (DSBMF), University Federico II of Napoli (UNINA), Biostructures and Bioimmages Institution (IBB), National Research Council (CNR); SDN Foundation (IRCCS). Naples, Italy
  • Carmine Mollica Department of Biomorphological and Functional Sciences (DSBMF), University Federico II of Napoli (UNINA), Biostructures and Bioimmages Institution (IBB), National Research Council (CNR); SDN Foundation (IRCCS). Naples, Italy
  • Massimo Imbriaco Department of Biomorphological and Functional Sciences (DSBMF), University Federico II of Napoli (UNINA), Biostructures and Bioimmages Institution (IBB), National Research Council (CNR); SDN Foundation (IRCCS). Naples, Italy
  • Mario Fusari Department of Biomorphological and Functional Sciences (DSBMF), University Federico II of Napoli (UNINA), Biostructures and Bioimmages Institution (IBB), National Research Council (CNR); SDN Foundation (IRCCS). Naples, Italy
  • Luigi Camera Department of Biomorphological and Functional Sciences (DSBMF), University Federico II of Napoli (UNINA), Biostructures and Bioimmages Institution (IBB), National Research Council (CNR); SDN Foundation (IRCCS). Naples, Italy
  • Marco Salvatore Department of Biomorphological and Functional Sciences (DSBMF), University Federico II of Napoli (UNINA), Biostructures and Bioimmages Institution (IBB), National Research Council (CNR); SDN Foundation (IRCCS). Naples, Italy
Keywords: Caroli Disease, Cholangiopancreatography, Magnetic Resonance, N, N'-bis(pyridoxal-5-phosphate)ethylenediamine-N, N'-diacetic acid, Pancreas

Abstract

Context Caroli’s disease is a rare congenital disorder first described by Caroli in 1958. This abnormality consists of non-obstructive, saccular or fusiform dilation of the intrahepatic bile ducts resulting in cystic lesions; similar abnormalities may also occur in the kidneys and pancreas. Case report We illustrate the role of enhanced mangafodipir trisodium magnetic resonance imaging in a patient with sporadic non-hereditary Caroli’s disease associated with pancreatic involvement in which mangafodipir trisodium magnetic resonance imaging characterized part of the cystic liver lesions as saccular dilations of the intrahepatic bile ducts of the left lobe, allowing diagnosis of the disease. Conclusion We strongly recommend hepatobiliary magnetic resonance imaging with mangafodipir trisodium in such patients.

Image: Hydrographic imaging.

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Hydrographic imaging
Published
2010-09-06
How to Cite
MaureaS., MollicaC., ImbriacoM., FusariM., CameraL., & SalvatoreM. (2010). Magnetic Resonance Cholangiography with Mangafodipir Trisodium in Caroli’s Disease with Pancreas Involvement. JOP. Journal of the Pancreas, 11(5), 460-463. https://doi.org/10.6092/1590-8577/3435