En Bloc Resection of the Pancreatic Head and Second Part of Duodenum for a Duodenal Gastrointestinal Stromal Tumor: A Multi-Media Report

  • Adam E Frampton Hepato-Pancreato-Biliary Surgical Unit, Department of Surgery and Cancer, Imperial College, Hammersmith Hospital Campus. London, United Kingdom
  • Jan J Bong Department of Surgery, National University of Malaysia. Bangi, Selangor, Malaysia
  • Charis Kyriakides Hepato-Pancreato-Biliary Surgical Unit, Department of Surgery and Cancer, Imperial College, Hammersmith Hospital Campus. London, United Kingdom
  • Patrizia Cohen Department of Histopathology, Imperial College NHS Trust, Charing Cross Hospital. London, United Kingdom
  • Long R Jiao Hepato-Pancreato-Biliary Surgical Unit, Department of Surgery and Cancer, Imperial College, Hammersmith Hospital Campus. London, United Kingdom
Keywords: Duodenum, Gastrointestinal Stromal Tumors, Pancreaticoduodenectomy

Abstract

Duodenal gastrointestinal stromal tumors are rare tumors. When these tumors arise from the second part of the duodenum they can easily be misdiagnosed as a pancreatic head cancer. A case of a 37-year-old female presenting with a one-year history of right upper quadrant pain is described here, who was subsequently found to have a mass in the head of the pancreas. Computed tomography scans showed a 2 cm hypervascular lesion lying between the head of pancreas and the second part of the duodenum, suggestive of a neuroendocrine tumor, and confirmed by endoscopic ultrasound scan. She underwent a pancreatic head resection with duodenal segmentectomy. Histopathological and immunohistochemical analysis revealed the tumor to be peri-ampullary duodenal gastrointestinal stromal tumor not invading the pancreas. Duodenal gastrointestinal stromal tumor can have a wide spectrum of clinical presentation. The accurate diagnosis of duodenal gastrointestinal stromal tumor is essential for determining the appropriate surgical intervention. In our case, a conservative surgical approach was utilised therefore avoiding a formal pancreaticoduodenectomy.

Image: Excision of the second part of duodenum.

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References

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Excision of the second part of duodenum
Published
2010-07-05
How to Cite
FramptonA., BongJ., KyriakidesC., CohenP., & JiaoL. (2010). En Bloc Resection of the Pancreatic Head and Second Part of Duodenum for a Duodenal Gastrointestinal Stromal Tumor: A Multi-Media Report. JOP. Journal of the Pancreas, 11(4), 396-400. https://doi.org/10.6092/1590-8577/3630
Section
MULTIMEDIA ARTICLES - Clinical Imaging and Video